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AMERICAN THORACIC SOCIETY
DOCUMENTS
Diagnosis of Idiopathic Pulmonary Fibrosis
An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline
Ganesh Raghu, Martine Remy-Jardin, Jeffrey L. Myers, Luca Richeldi, Christopher J. Ryerson, David J. Lederer,
Juergen Behr, Vincent Cottin, Sonye K. Danoff, Ferran Morell, Kevin R. Flaherty, Athol Wells, Fernando J. Martinez,
Arata Azuma, Thomas J. Bice, Demosthenes Bouros, Kevin K. Brown, Harold R. Collard, Abhijit Duggal, Liam Galvin,
Yoshikazu Inoue, R. Gisli Jenkins, Takeshi Johkoh, Ella A. Kazerooni, Masanori Kitaichi, Shandra L. Knight,
´
George Mansour, Andrew G. Nicholson, Sudhakar N. J. Pipavath, Ivette Buendıa-Roldan,´ Moises´ Selman,
William D. Travis, Simon Walsh, and Kevin C. Wilson; on behalf of the American Thoracic Society, European
Respiratory Society, Japanese Respiratory Society, and Latin American Thoracic Society
THIS OFFICIAL CLINICAL PRACTICE GUIDELINE OF THE AMERICAN THORACIC SOCIETY (ATS), EUROPEAN RESPIRATORY SOCIETY (ERS), JAPANESE RESPIRATORY
SOCIETY (JRS), AND LATIN AMERICAN THORACIC SOCIETY (ALAT) WAS APPROVED BY THE ATS, JRS, AND ALAT MAY 2018, AND THE ERS JUNE 2018
Background: This document provides clinical recommendations diagnosis, conditional recommendations were made for performing
for the diagnosis of idiopathic pulmonary fibrosis (IPF). It represents BAL and surgical lung biopsy; because of lack of evidence, no
a collaborative effort between the American Thoracic Society, recommendation was made for or against performing transbronchial
European Respiratory Society, Japanese Respiratory Society, and lung biopsy or lung cryobiopsy. In contrast, for patients with newly
Latin American Thoracic Society.
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