儿童肺先天性囊性腺瘤样畸形23例的临床病理分析解析新.pdf

，U 儿童肺先天性囊性腺瘤样畸形23例的临床病理分析 王雪莉史青奚政君张彬王佳 【摘要】目的探讨儿童肺先天性囊性腺瘤样畸形(CCAM)的临床、病理学特征及鉴别诊断要点。方法对23例经手术、 病理证实的CCAM进行临床病理分析，并系统复习文献，讨论其发病机制、病理分型、临床特点、治疗和预后。结果23例 CCAM中男女发病机会基本相同，年龄2个月-12岁，均累及单侧单叶肺，其中CCAM 与肺隔离症、支气管源囊肿、先天性肺气肿等鉴别。CCAM患者常伴有感染等并发症，并有一定的恶变风险，手术切除病变 肺叶是有效的治疗方法。 【关键词】先天性囊性腺瘤样畸形；肺；囊肿 of23 adenomatoid Clinicopathologicanalysiscongenitalcystic malformationof inchildhood lung Xue Jia WANGli，SHI Bin，WANG Qing，xIZhengjun，ZHANG Children’s Affiatedto ．Departmentofpathology,ShanghaiHospital ShanghaiJiaotongUniversity Todiscusstheclinic featuresanddifferential of cystic Abstract：Purpose pathomorphologic diagnosiscongenital adenomatoid thechildren．MethodsTheclinicaland wereevaluated malformation(CCAM)of pathologicfindings in23casesofCCAMconfirmed and byoperationpathologicanalysis，Thepathogenesis，pathological clinicalfeatures．treatmentand werediscussed1aterwithreviewoftherelated1iterature。ResultsCCAMhas prognosis nosex from2monthsto12 involvedunilateraland lobeinaU23 predilection．Patientageranged years．Lesions single 17casesofCCAM casesofCCAM 2casesofCCAM patients，including typeI(73．9％)，4 type，(17．4％)and type，(8．7％)． ConclusionsCCAMiSarare malformationof istheefectivemethodtodetect congenital lung．Imaging the on differential other diagnosisdependspathologicalexamination，Thediagnosisencompassescongenital